Hereditary Fructose Intolerance and
A Fructose Free Diet

Hereditary fructose intolerance is a disorder that your born with and it may strike more people of European descent or Caucasian people

This disorder can strike about 1 in 20,000 people which makes it a somewhat common health problem. 

This will lead to fructose metabolism problems which can create unpleasant as well as very serious health issues. 

The only way to deal with a serious fructose metabolism problem created by hereditary fructose intolerance may be to adopt a fructose free diet.

It's a Genetic Disorder

This is a genetic disorder that you were born with and it can be inherited from someone in your family - like your parents.

The people that have hereditary fructose intolerance will not be able to properly metabolize fructose. 

This is due to a deficiency of a particular liver enzyme which converts fructose into glucose.  Which will end up being a big problem for people with this genetic disorder these days.

Fructose Metabolism Problems

Normally, fructose is absorbed through your small intestine and is then sent to your liver to be converted into glucose.

However, when your liver is missing "the" particular "enzyme", fructose can no longer be converted and you will experience fructose metabolism problems.

This will put a huge strain on your body, especially your liver and kidneys!

When fructose can't be converted, it will then start to accumulate in your body and this may result in Acidosis. 

Attempts to deal with this unusable sugar create toxic substances such as uric acid and severe abdominal pain.  Vomiting may soon follow the ingestion of fructose.

Symptoms of Hereditary Fructose Intolerance or (HFI)

  • Abdominal Pain & Bloating
  • Flatulence
  • Vomiting
  • Diarrhea
  • Extreme Thirst
  • Excessive Sweating
  • Excessive Sleepiness
  • Irritability
  • Failure to Grow
  • Weight Loss
  • Hypoglycemia
  • Convulsions
  • Acidosis
  • Excessive Urination
  • Fatigue
  • Fever
  • Depression
  • Jaundice
  • Enlarged Liver
  • Kidney Problems

If you think that you suffer from a fructose metabolism problem like HFI, pay attention to what happens after eating fruit or other foods that contain an ample amount of fructose.


Tests Used to Diagnose
Hereditary Fructose Intolerance

  • Enzyme Tests
  • Urine Tests
  • Blood Tests
  • Fructose Tolerance Test
  • Liver Biopsy

And if you suspect that you can't digest fructose - have it checked out by someone licensed to do this type of testing.

The Fructose Free Diet Excludes:

  • Most Fruits (especially dried)
  • Fructose Sugar
  • Fruit Syrup
  • Fruit Juice Concentrate
  • Preserves
  • Tomato Concentrate
  • Beetroot
  • Sweet Onions
  • Cabbage
  • Artichoke
  • Cauliflower
  • Sugar Snap Peas
  • White Sugar or Table Sugar
  • Invert Sugar
  • Brown Sugar
  • Raw Sugar
  • Honey
  • Palm Sugar
  • Coconut Sugar
  • Turbinado Sugar
  • Molasses
  • Maple Syrup
  • Cane Sugar
  • Jaggery
  • Agave Syrup & Nectar
  • High Fructose Corn Syrup
  • Corn Syrup Solids
  • Sugar Alcohols (sorbitol, xylitol, erythritol, etc.)

*Even though a sugar alcohol does not actually contain fructose - it can affect your body similarly to fructose.

A Safe Fructose Free Diet Includes:

Healthy Proteins:  Wild Caught Shellfish, Wild Caught Fish, Grass Fed Meats, Game Meats, Pastured Poultry, and Pastured Pork

Eggs:  Pastured Chicken Eggs (with bright orange egg yolks), Duck Eggs, Quail Eggs, and Fish Eggs or Caviar

Grass Fed Dairy:  Raw Whole Milk, Raw Butter, Unsweetened Yogurt, Raw Cream, Sour Cream, Cottage Cheese, and Raw Cheese

Oils:  Extra Virgin Olive Oils, Organic Macadamia Nut Oil, Virgin Coconut Oils, Virgin Avocado Oil, and Cold Pressed Flax Seed Oil

Nuts:  Walnuts, Pecans, Mature Coconuts, Macadamia Nuts, Pine Nuts, Almonds, Brazil Nuts, and Hazelnuts

Seeds:  Sunflower Seeds, Flax Seeds, Chia Seeds, Pumpkin Seeds, and Sesame Seeds

Grains:  White Rice, Brown Rice, Amaranth, Rye, Buckwheat, Barley, Millet, and Sorghum

Legumes:  Kidney Beans, Pinto Beans, Navy Beans, Cashews, and Peanuts

Herbs:  Thyme, Basil, Oregano, Mint, Bay Leaf, Marjoram, Parsley, Cilantro, and Rosemary

Could be Safe for a Fructose Free Diet

Vegetables:  Boston Lettuce, Red Leaf Lettuce, Green Leaf Lettuce, Romaine Lettuce, Celery, Spinach, Mushrooms, Radishes, and Alfalfa Sprouts

Fruit:  Avocados, Lemons, Lemon Juice, Limes, Lime Juice, and Jalapeno Peppers

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