Hereditary Fructose Intolerance and
A Fructose Free Diet

Hereditary fructose intolerance is a disorder that you are born with and may strike more people of European descent or Caucasian people.

This will lead to fructose metabolism problems which can create unpleasant as well as very serious health issues.  This disorder can strike about 1 in 20,000 people which makes it a somewhat common health problem.

And the only way to deal with a serious fructose metabolism problem created by hereditary fructose intolerance may be to adopt a fructose free diet.

You Were Born With This Problem!

This is a genetic disorder that you were born with and it can be inherited from someone in your family - like your parents.

And the people that have Hereditary fructose intolerance will not be able to properly metabolize fructose.  This is due to a deficiency of a particular liver enzyme which converts fructose into glucose.

Which will end up being a big problem for people with this disorder - especially these days.

Fructose Metabolism Problems

Normally, Fructose is absorbed through your small intestine and is then sent to your liver to be converted into glucose.

But, when your liver is missing "the" particular enzyme, fructose can no longer be converted and you will experience fructose metabolism problems.

This will put a huge strain on your body, especially your liver and kidneys!

Because this fructose can't be converted, it will then start to accumulate in your body and may result in Acidosis.

Attempts to deal with this unusable sugar, create toxic substances such as uric acid and severe abdominal pain as well as vomiting may soon follow the ingestion of fructose.

Symptoms of Hereditary Fructose Intolerance or (HFI)

  • Abdominal Pain
  • Bloating
  • Flatulence
  • Vomiting
  • Diarrhea
  • Extreme Thirst
  • Excessive Sweating
  • Excessive Urination
  • Fatigue
  • Fever
  • Depression
  • Excessive Sleepiness
  • Irritability
  • Failure to Grow
  • Weight Loss
  • Jaundice
  • Enlarged Liver
  • Kidney Problems
  • Hypoglycemia
  • Convulsions
  • Acidosis

The Fructose Free Diet Excludes:

  • Fructose Sugar
  • Sucrose
  • Sorbitol
  • Honey
  • Maple Syrup
  • Agave Syrup
  • Fruit Syrup
  • Invert Sugar
  • High Fructose Corn Syrup
  • Fruits
  • Vegetables like Eggplant, Cabbage, and Sweet Onions

*Even though sorbitol is a sugar alcohol and does not actually contain fructose - it can affect your body similarly to what fructose can do.

A Safe Fructose Free Diet Includes:

Wild Caught Fish, Wild Caught Seafood, Grass Fed Meats, Game Meats, and Sustainable Pork

Pastured Chicken Eggs (with bright orange egg yolks), Pastured Poultry, and Other Types of Eggs

Nuts like Walnuts, Pecans, Mature Coconuts, Macadamia Nuts, Almonds, Brazil Nuts, and Hazelnuts

Oils like Unrefined Coconut Oil, Unrefined Macadamia Nut Oil, Unrefined Olive Oil. and Unrefined Flax Seed Oil

Grains like Rice, Amaranth, Buckwheat, and Barley

Legumes like Peanuts, Kidney Beans, and Pinto Beans

Dairy such as Whole Milk, Butter, Unsweetened Yogurt, Cream, Sour Cream, Cottage Cheese, and Cheese

Seeds like Sunflower Seeds, Flax Seeds, and Pumpkin Seeds

May also be Safe for a Fructose Free Diet

Vegetables like Green Leaf Lettuce, Red Leaf Lettuce, Boston Lettuce, Romaine Lettuce, Celery, Various Mushrooms, Spinach, Asparagus, Brussel Sprouts, Alfalfa Sprouts, Okra, and Radishes

Fruit like Lemons, Limes, Green Peppers, and Jalapeno Peppers


Tests Used to Diagnose
Hereditary Fructose Intolerance

  • Enzyme Tests
  • Urine Tests
  • Blood Tests
  • Fructose Tolerance Test
  • Liver Biopsy

If you think that you suffer from a fructose metabolism problem like HFI, pay attention to what happens after eating fruit or other foods that contain an ample amount of fructose.

And if you suspect that you can't digest fructose - have it checked out by someone licensed to do this type of testing.


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